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KMID : 0605919960020020151
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Journal of Korean Association of Pediatric Surgeons
1996 Volume.2 No. 2 p.151 ~ p.0
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Colon Perforation in Hyperimmunoglobulin E Syndrome
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오정탁
기인규/한석주/김호근/황의호
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Abstract
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Hyperimmunoglobulin E syndrome is a relatively rare primary immunodeficiency syndrome characterized by recurrent infection, abscess formation and marked elevation of serum IgE level. The common infectious organism is Staphylococcus aureus and
recurrent
infection indicates some defects in the immunologic system. Although the infection can affect various organs, gastrointestinal tract involvement is rare and only one case of colon perforation has been previously reproted. Herein we report another
one
case of colon perforation which ocurred in an 8-year-old girl with hyperimmunoglobulin E syndrome. The patient was admitted to the hospital due to an abscess on right neck. The diagnosis of hyperimmunoglobulin E syndrom was made because she had
eczematoid dermatitis on the face, pneumatocele on left upper lung field and markedlh elevated serum Ig E level(>15,000 IU/ml) with a past histories of frequent scalp abscesses and otitis media. Abdominal pain deveoloped on the 13th day of
admission and
abdominal plain X-ray revealed free air. An exploratory lapartomy was performed and two free perforations of the transverse colon were noted. Segmental resection and double barrel colostomy were performed. Colostomy closure was done 4 month later
and
she had no. gastrointestinal problem during a follow up period of 12 months.
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